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Laboratory diagnosis and management of von Willebrand disease in South Africa
(Thieme Medical Publishers, 2011)
Patients with von Willebrand disease (VWD) in South Africa are cared for in
17 Hemophilia Treatment Centers. The exact prevalence of the disease is uncertain, but
539 patients are annotated in registries. VWD patients ...
Differential sensitivity of von Willebrand factor (VWF) 'activity' assays to large and small VWF molecular weight forms: a cross-laboratory study comparing ristocetin cofactor, collagen-binding and mAb-based assays
(International Society on Thrombosis and Haemostasis, 2012)
Background: von Willebrand disease (VWD), the
most common inherited bleeding disorder, is caused by
deficiencies and/or defects in von Willebrand factor (VWF).
An effective diagnostic and VWD typing strategy requires
plasma ...